Xanthoma disseminatum (xanthogranuloma disseminatum)
2019年3月13日 · Xanthoma disseminatum (XD) is a rare, normolipemic form of histiocytosis. Patients rapidly develop hundreds of red-brown papules that become increasingly yellow with time. The lesions are symmetrically distributed and involve the eyelids, trunk, face, and flexural folds of the proximal extremities.
Xanthoma disseminatum | About the Disease | GARD - Genetic …
Xanthoma disseminatum is a rare disease that affects multiple areas of the body. It causes yellowish-red or brown bumps on the skin and inside the mouth and nose. Sometimes, it can also affect organs and parts of the brain like the pituitary gland and hypothalamus which release hormones in the body to regulate various body functions.
Xanthoma disseminatum - an overview | ScienceDirect Topics
Xanthoma disseminatum is a rare and unusual disease characterized by xanthomatous nodules in the axillae, the antecubital and popliteal fossae, the intertriginous areas, and the oropharynx and upper respiratory tract.
Xanthoma disseminatum - Wikipedia
Xanthoma disseminatum is a rare cutaneous condition that preferentially affects males in childhood, characterized by the insidious onset of small, yellow-red to brown papules and nodules that are discrete and disseminated.
Xanthoma Disseminatum | JAMA Dermatology - JAMA Network
Xanthoma disseminatum is a normolipemic disseminated xanthomatosis that tends to localize on the flexural and intertriginous surfaces, is often associated with diabetes insipidus, and appears to run a chronic benign course.
Xanthoma - StatPearls - NCBI Bookshelf - National Center for ...
2023年8月28日 · Xanthomas are localized lipid deposits within an organ system. They are often an important sign of systemic disease. To avoid the high morbidity and mortality associated with the underlying systemic condition, it must be promptly diagnosed and treated.
Xanthoma disseminatum: report of one case - PMC - National …
2019年12月1日 · Xanthoma disseminatum, also known as Montgomery syndrome, is a rare non-Langerhans cell-derived benign histiocytosis disease with unknown etiology. The disease occurs most frequently in men, ranging in age from 8 months to 85 years, but 60% of patients develop the disease before the age of 25 years [ 2 ].
Xanthoma Disseminatum Presenting with Hoarseness - PMC
2016年6月1日 · Xanthoma disseminatum (XD) is a rare, benign, non-Langerhans cell histiocytic disorder with unknown etio-pathology. It manifests with multiple, grouped, red-brown to yellow papules and nodules involving the skin, mucous membranes, and internal organs with a predilection for flexures and the face.
Xanthoma disseminatum - The Lancet
2018年1月20日 · Xanthoma disseminatum is a rare normolipidaemic mucocutaneous xanthomatosis, characterised by proliferation of histiocytic cells and secondary deposition of lipid in the dermis, which can affect people of any age. The male to female ratio is 2·4:1.
Xanthoma Disseminatum : Effective Therapy With 2-Chlorodeoxyadenosine ...
Therapy with 2-chlorodeoxyadenosine was effective at inducing remission and long-term control of cutaneous lesions of xanthoma disseminatum in 5 cases. Adverse effects were minimal, and treatment was well tolerated.
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