Vasculitis refers to inflammation of the blood vessels leading to tissue destruction with or without organ damage. Vasculitis is classified as small vessel, medium vessel or large vessel vasculitis[1] and maybe either idiopathic or associated with an underlying pathology/disease.  Small vessel vascu...

Antineutrophilic cytoplasmic antibody (ANCA) associated vasculitides are a heterogeneous group of rare autoimmune conditions that causes an inflammation of blood vessels with various manifestations. It includes three main diseases, which are granulomatosis with polyangiitis (GPA; formerly known as W...

The many forms of vasculitis are characterized by inflammation of blood vessels, leading to potentially long-term sequelae including vision loss, aneurysm formation and kidney failure. Accurate estimation of the incidence and prevalence has been hampered by the absence of reliable diagnostic criteri...

Vasculitis is a heterogeneous group of pathologies characterized by inflammation of vessels. They share common links of clinical, laboratory, and pathophysiologic features. The clinical and pathological features are variable and depend on the site and type of blood vessels affected. Research has ide...

The vasculitides encompass a group of inflammatory conditions affecting the blood vessels with severe consequences including tissue ischemia, structural abnormalities, such as aneurysms/dissections, and end organ damage. The different forms are commonly classified based on the size of the blood vess...

Systemic vasculitis is a term that covers a group of rare conditions characterized by inflammation of blood vessels, which leads to organ ischaemia and damage. Vasculitis can affect individuals of all ages, but certain conditions show a marked age tropism; for example, Kawasaki disease affects young...

Systemic vasculitis can be a challenge to differentiate from other forms of vasculopathy. Because treatment for systemic vasculitis is disparate from that for other forms of vasculopathy, clinicians should strive for high diagnostic certainty. This review article aims to highlight the clinical, radi...

Vasculitis is defined by the presence of blood vessel inflammation. It can be observed in a wide variety of settings, which can be broadly grouped as secondary vasculitides, which occur in association with an underlying disease or trigger, or primary vasculitides, in which vasculitis is occurring fo...

Immunoglobulin A vasculitis (IgAV), formerly Henoch-Schönlein purpura, involves the small vessels of the joints, kidneys, gastrointestinal tract, and skin. IgAV can also affect the central nervous system and the lungs; however, these findings are rare. It is an acute IgA-mediated disorder typically ...

The recent publication of the American College of Rheumatology (ACR)-European Alliance of Associations for Rheumatology (EULAR) classification criteria for large vessel vasculitis and anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitides (AAVs) has provided modern criteria for the clas...

Vasculitides, characterized by inflammation and damage of blood vessels, encompass a broad spectrum of diseases. They can occur with different pathophysiological mechanisms and have a rich clinical heterogeneity depending on the vessel diameters they affect. Vasculitides may also present with a broa...

Large- and small-vessel vasculitis are complex potentially life-threatening systemic autoimmune diseases that have recently been subjected to considerable immunologic and clinical research. Following the other reviews of this series, here we aim to summarise some of the most significant studies that...